Friday, September 20, 2019
Home > News > Surgeons chip away at the cheekbones of man with ‘lion face syndrome’

Surgeons chip away at the cheekbones of man with ‘lion face syndrome’

A man whose face bones grew too big because of a rare condition known ‘lion face syndrome’ needed surgery to chip off parts of his skull.

The patient known only as Suresh, from Tamil Nadu in the south of India, was given the operation for free by generous surgeons.

To have the condition this severe is extremely rare, Suresh’s doctor said, and there are thought to have only been a few cases ever documented.

Suresh spent half his life living with the condition after it began when he was 18 years old, until he desperately began seeking medical help 20 years later.

 

The 41-year-old man, Suresh, lived for around 20 years before he began seeking help for the condition which caused his face bones to grow uncontrollably large

Suresh was eventually helped by surgeons in his home state of Tamil Nadu who reduced the bones' size

The 41-year-old man, Suresh, lived for around 20 years before he began seeking help for the condition which caused his face bones to grow uncontrollably large (left), but was eventually helped by surgeons in his home state of Tamil Nadu who reduced the bones’ size (right)

Suresh has leontiasis ossea, also known as lion face syndrome, which causes the bones in the face to grow too large.

It caused his jaw to swell painfully large and his cheek bones became huge and protruded sideways out of his face.

The bridge of his nose was also left smaller by the condition, while his eye sockets were deepened because of the build up of bone around them.

He had lived a normal life until he was 18 years old and signs of the condition began to appear. 

Suresh spent 10 days in hospital after his operation but was given his treatment for free, only paying for medications because he was poor

Surgeons successfully managed to reduce the size of the bones around Suresh's eyes

Suresh spent 10 days in hospital after his operation but was given his treatment for free, only paying for medications because he was poor – surgeons successfully managed to reduce the size of the bones around his eyes

Dr Sunil Richardson, who carried out the surgery, said it was very rare to see someone with such a severe form of the condition

Dr Sunil Richardson, who carried out the surgery, said it was very rare to see someone with such a severe form of the condition

Lion face syndrome is so named because, untreated, it is thought to give patients a face similar to that of a lion.    

The condition cannot be stopped and can only be treated by cutting the skin to expose the overgrown bones and chip away at them.

Thanks to his surgeon, Dr Sunil Richardson in Nagercoil, a city at the southern tip of India, Suresh’s face is now completely transformed.

Dr Richardson said: ‘This patient had visited more than a dozen surgeons in different cities seeking treatment and all of the doctors only delayed it. 

‘He heard about our craniofacial work through another patient and then came over.

‘Since he was a poor patient, we treated him for free and he only paid for his medicines.

‘Surgical treatment is the only effective choice and we did a cosmetic shave of the lesion without leaving an obvious scar.’ 

In post-surgery photos, Suresh – whose name has been changed for privacy reasons – appears completely different.

WHAT IS LION FACE SYNDROME? 

Lion face syndrome is a name for a rare condition called leontiasis ossea, in which bones in the face grow too large.

It is a complication of fibrous dysplasia, which is more common.

Fibrous dysplasia is a condition present from birth which is caused by a genetic mutation and is not inherited.

It causes bones to be replaced with connective tissue which can weaken them and make them more likely to grow too large.

It can be treated with medication to strengthen bones and surgery to remove unwanted growths.

Source: Head and Face Medicine and Great Ormond Street Hospital

Dr Richarson, 42, said the patient’s condition was a result of fibrous dysplasia, where normal bone is replaced with connective tissue.  

Fibrous dysplasia is a genetic condition which people are born with and is caused by a genetic mutation early on in the pregnancy – it is not hereditary.

Early signs can include a swollen jaw and teeth which are far apart. In rare cases the condition can affect hearing or vision if bones grow and press on the eyes and ears. 

It leads to bones which are weak and prone to expanding, which in turn can cause leontiasis ossea.

‘It’s a very, very rare condition and – as this case is true classical leontiasis ossea – it is even more rare,’ he added. 

‘There are maybe a few ever published in literature.’ 

Suresh spent a total of 10 days in hospital, including one in intensive care, in Nagercoil.

Left untreated, lion face syndrome can encroach on the eyes, mouth and nose, interfering with sight, breathing and the taking of food. 

In extreme cases, it can lead to the senses being lost one by one before death caused by pressure on the brain. 

Read more at DailyMail.co.uk